NDUFS6, Unconjugated, Rabbit

Catalog Number: NBS-BT-FONZE7-100
Article Name: NDUFS6, Unconjugated, Rabbit
Biozol Catalog Number: NBS-BT-FONZE7-100
Supplier Catalog Number: BT-FONZE7-100
Alternative Catalog Number: NBS-BT-FONZE7-100
Manufacturer: Nordic BioSite
Host: Rabbit
Category: Antikörper
Application: WB
Species Reactivity: Human, Mouse, Rat
Immunogen: Synthetic peptide, corresponding Human NDUFS6.
Conjugation: Unconjugated
Alternative Names: NADH dehydrogenase [ubiquinone] iron-sulfur protein 6, mitochondrial, Complex I-13kD-A, CI-13kD-A, NADH-ubiquinone oxidoreductase 13 kDa-A subunit
NDUFS6 a complex I subunit gene not previously associated with complex I deficiency, was grossly underexpressed in the 2 patient cell lines. Both patients had homozygous mutations in this gene, one causing a splicing abnormality and the other a large del
Clonality: Polyclonal
Molecular Weight: ~ 13 kDa
UniProt: O75380
Buffer: Rabbit IgG, 1mg/ml in PBS with 0.02% sodium azide, 50% glycerol, pH7.2
Source: rabbit
Purity: The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen and the purity is > 95% (by SDS-PAGE).
Antibody Type: Primary Antibody
Application Notes: WB: 1:500~1:1000